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Outside in: the matrix as a modifier of muscular dystrophy

Muscular dystrophies are genetic conditions leading to muscle degeneration and often, impaired regeneration. Duchenne Muscular Dystrophy is a prototypical form of muscular dystrophy, and like other forms of genetically inherited muscle diseases, pathological progression is variable. Variability in m...

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Detalles Bibliográficos
Publicado en:Biochim Biophys Acta
Autores principales: Quattrocelli, Mattia, Spencer, Melissa J., McNally, Elizabeth M.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2016
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5262521/
https://ncbi.nlm.nih.gov/pubmed/28011285
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbamcr.2016.12.020
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