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Hemophagocytic lymphohistiocytosis in adults: An under recognized entity

Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of severe immune activation with macrophage and T-cell infiltration resulting in, multi organ damage. HLH may be primary or secondary in etiology. A high index of suspicion is essential for early diagnosis and treatment. Diagnostic criteria need...

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Detalhes bibliográficos
Publicado no:BBA Clin
Main Authors: Shah, Abdul Rashid, Muzzafar, Tariq, Assi, Rita, Schellingerhout, Dawid, Estrov, Zeev, Tamamyan, Gevorg, Kantarjian, Hagop, Daver, Naval
Formato: Artigo
Idioma:Inglês
Publicado em: Elsevier 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5219626/
https://ncbi.nlm.nih.gov/pubmed/28070498
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbacli.2016.12.002
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