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Oxidative metabolism and Ca(2+) handling in isolated brain mitochondria and striatal neurons from R6/2 mice, a model of Huntington’s disease

Alterations in oxidative metabolism and defects in mitochondrial Ca(2+ )handling have been implicated in the pathology of Huntington’s disease (HD), but existing data are contradictory. We investigated the effect of human mHtt fragments on oxidative metabolism and Ca(2+ )handling in isolated brain m...

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Bibliografske podrobnosti
izdano v:Hum Mol Genet
Main Authors: Hamilton, James, Pellman, Jessica J., Brustovetsky, Tatiana, Harris, Robert A., Brustovetsky, Nickolay
Format: Artigo
Jezik:Inglês
Izdano: Oxford University Press 2016
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC5181640/
https://ncbi.nlm.nih.gov/pubmed/27131346
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddw133
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