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Familial Mediterranean fever presenting as fever of unknown origin in Korea

Familial Mediterranean fever (FMF) is the most common Mendelian autoinflammatory disease, characterized by uncontrolled activation of the innate immune system that manifests as recurrent brief fever and polyserositis (e.g., peritonitis, pleuritic, and arthritis). FMF is caused by autosomal recessive...

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Detalles Bibliográficos
Publicado en:Korean J Pediatr
Main Authors: Lee, Jun Hee, Kim, Jong Hyun, Shim, Jung Ok, Lee, Kwang Chul, Lee, Joo Won, Lee, Jung Hwa, Chae, Jae Jin
Formato: Artigo
Idioma:Inglês
Publicado: The Korean Pediatric Society 2016
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5177713/
https://ncbi.nlm.nih.gov/pubmed/28018446
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3345/kjp.2016.59.11.S53
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