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Familial Mediterranean fever presenting as fever of unknown origin in Korea
Familial Mediterranean fever (FMF) is the most common Mendelian autoinflammatory disease, characterized by uncontrolled activation of the innate immune system that manifests as recurrent brief fever and polyserositis (e.g., peritonitis, pleuritic, and arthritis). FMF is caused by autosomal recessive...
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| Publicado no: | Korean J Pediatr |
|---|---|
| Main Authors: | , , , , , , |
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
The Korean Pediatric Society
2016
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| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5177713/ https://ncbi.nlm.nih.gov/pubmed/28018446 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3345/kjp.2016.59.11.S53 |
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