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Orbital/Peri-Orbital Plexiform Neurofibromas in Children with Neurofibromatosis type 1: Multi-disciplinary Recommendations for Care

Children and adults with Neurofibromatosis type 1 (NF1), a common autosomal dominant condition, manifest a variety of ophthalmologic conditions. Plexiform neurofibromas involving the eyelid, orbit, periorbital and facial structures (termed OPPN) can result in significant visual loss in children. Equ...

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Dades bibliogràfiques
Publicat a:Ophthalmology
Autors principals: Avery, Robert A., Katowitz, James A., Fisher, Michael J., Heidary, Gena, Dombi, Eva, Packer, Roger J., Widemann, Brigitte C.
Format: Artigo
Idioma:Inglês
Publicat: 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5173440/
https://ncbi.nlm.nih.gov/pubmed/27817916
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ophtha.2016.09.020
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