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Validation of ultrasonography for non‐invasive assessment of diaphragm function in muscular dystrophy

KEY POINTS: Duchenne muscular dystrophy (DMD) is a severe, degenerative muscle disease that is commonly studied using the mdx mouse. The mdx diaphragm muscle closely mimics the pathophysiological changes in DMD muscles. mdx diaphragm force is commonly assessed ex vivo, precluding time course studies...

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Detalhes bibliográficos
Publicado no:J Physiol
Main Authors: Whitehead, Nicholas P., Bible, Kenneth L., Kim, Min Jeong, Odom, Guy L., Adams, Marvin E., Froehner, Stanley C.
Formato: Artigo
Idioma:Inglês
Publicado em: John Wiley and Sons Inc. 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5157096/
https://ncbi.nlm.nih.gov/pubmed/27570057
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1113/JP272707
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