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Brain inflammation is accompanied by peripheral inflammation in Cstb(−/−) mice, a model for progressive myoclonus epilepsy

Progressive myoclonus epilepsy of Unverricht-Lundborg type (EPM1) is an autosomal recessively inherited childhood-onset neurodegenerative disorder, characterized by myoclonus, seizures, and ataxia. Mutations in the cystatin B gene (CSTB) underlie EPM1. The CSTB-deficient (Cstb (−/−)) mouse model rec...

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Dades bibliogràfiques
Publicat a:J Neuroinflammation
Autors principals: Okuneva, Olesya, Li, Zhilin, Körber, Inken, Tegelberg, Saara, Joensuu, Tarja, Tian, Li, Lehesjoki, Anna-Elina
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5127053/
https://ncbi.nlm.nih.gov/pubmed/27894304
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12974-016-0764-7
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