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Electromyographic evidence in support of a knock-in mouse model of DYT1 dystonia

BACKGROUND: DYT1 dystonia is an autosomal dominant movement disorder characterized by abnormal, often repetitive, movements, and postures. Its hallmark feature is sustained or intermittent contractions of muscles involving co-contractions of antagonist muscle pairs. The symptoms are relieved with th...

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Publicat a:Mov Disord
Autors principals: DeAndrade, Mark P., Trongnetrpunya, Amy, Yokoi, Fumiaki, Cheetham, Chad C., Peng, Ning, Wyss, J. Michael, Ding, Mingzhou, Li, Yuqing
Format: Artigo
Idioma:Inglês
Publicat: 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5115930/
https://ncbi.nlm.nih.gov/pubmed/27241685
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/mds.26677
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