Загрузка...

Mutations in the liver glycogen synthase gene in children with hypoglycemia due to glycogen storage disease type 0.

Glycogen storage disease type 0 (GSD-0) is a rare form of fasting hypoglycemia presenting in infancy or early childhood and accompanied by high blood ketones and low alanine and lactate concentrations. Although feeding relieves symptoms, it often results in postprandial hyperglycemia and hyperlactat...

Полное описание

Сохранить в:
Библиографические подробности
Главные авторы: Orho, M, Bosshard, N U, Buist, N R, Gitzelmann, R, Aynsley-Green, A, Blümel, P, Gannon, M C, Nuttall, F Q, Groop, L C
Формат: Artigo
Язык:Inglês
Опубликовано: 1998
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC508911/
https://ncbi.nlm.nih.gov/pubmed/9691087
Метки: Добавить метку
Нет меток, Требуется 1-ая метка записи!