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Newborn Cystic Fibrosis Pigs Have a Blunted Early Response to an Inflammatory Stimulus

Rationale: Studies suggest that inappropriate responses to proinflammatory stimuli might contribute to inflammation in cystic fibrosis (CF) lungs. However, technical challenges have made it difficult to distinguish whether altered responses in CF airways are an intrinsic defect or a secondary effect...

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Bibliographic Details
Published in:Am J Respir Crit Care Med
Main Authors: Bartlett, Jennifer A., Ramachandran, Shyam, Wohlford-Lenane, Christine L., Barker, Carrie K., Pezzulo, Alejandro A., Zabner, Joseph, Welsh, Michael J., Meyerholz, David K., Stoltz, David A., McCray, Paul B.
Format: Artigo
Language:Inglês
Published: American Thoracic Society 2016
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Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC5074652/
https://ncbi.nlm.nih.gov/pubmed/27027566
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1164/rccm.201510-2112OC
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