A carregar...

Hepatic and neuromuscular forms of glycogen storage disease type IV caused by mutations in the same glycogen-branching enzyme gene.

Glycogen storage disease type IV (GSD-IV) is an autosomal recessive disease resulting from deficient glycogen-branching enzyme (GBE) activity. The classic and most common form is progressive liver cirrhosis and failure leading to either liver transplantation or death by 5 yr of age. However, the liv...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Main Authors: Bao, Y, Kishnani, P, Wu, J Y, Chen, Y T
Formato: Artigo
Idioma:Inglês
Publicado em: 1996
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC507139/
https://ncbi.nlm.nih.gov/pubmed/8613547
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!