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Zfp423 Regulates Sonic Hedgehog Signaling via Primary Cilium Function

Zfp423 encodes a 30-zinc finger transcription factor that intersects several canonical signaling pathways. Zfp423 mutations result in ciliopathy-related phenotypes, including agenesis of the cerebellar vermis in mice and Joubert syndrome (JBTS19) and nephronophthisis (NPHP14) in humans. Unlike most...

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Publicat a:PLoS Genet
Autors principals: Hong, Chen-Jei, Hamilton, Bruce A.
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5065120/
https://ncbi.nlm.nih.gov/pubmed/27727273
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pgen.1006357
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