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A human in vitro model of Duchenne muscular dystrophy muscle formation and contractility

Tongue weakness, like all weakness in Duchenne muscular dystrophy (DMD), occurs as a result of contraction-induced muscle damage and deficient muscular repair. Although membrane fragility is known to potentiate injury in DMD, whether muscle stem cells are implicated in deficient muscular repair rema...

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Detalhes bibliográficos
Publicado no:J Cell Biol
Main Authors: Nesmith, Alexander P., Wagner, Matthew A., Pasqualini, Francesco S., O’Connor, Blakely B., Pincus, Mark J., August, Paul R., Parker, Kevin Kit
Formato: Artigo
Idioma:Inglês
Publicado em: The Rockefeller University Press 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5057287/
https://ncbi.nlm.nih.gov/pubmed/27697929
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.201603111
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