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Defective fluid shear stress mechanotransduction mediates hereditary hemorrhagic telangiectasia

Morphogenesis of the vascular system is strongly modulated by mechanical forces from blood flow. Hereditary hemorrhagic telangiectasia (HHT) is an inherited autosomal-dominant disease in which arteriovenous malformations and telangiectasias accumulate with age. Most cases are linked to heterozygous...

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Detaylı Bibliyografya
Yayımlandı:J Cell Biol
Asıl Yazarlar: Baeyens, Nicolas, Larrivée, Bruno, Ola, Roxana, Hayward-Piatkowskyi, Brielle, Dubrac, Alexandre, Huang, Billy, Ross, Tyler D., Coon, Brian G., Min, Elizabeth, Tsarfati, Maya, Tong, Haibin, Eichmann, Anne, Schwartz, Martin A.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: The Rockefeller University Press 2016
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC5037412/
https://ncbi.nlm.nih.gov/pubmed/27646277
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.201603106
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