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Monogenic polyarteritis: the lesson of ADA2 deficiency

The deficiency of Adenosine Deaminase 2 (DADA2) is a new autoinflammatory disease characterised by an early onset vasculopathy with livedoid skin rash associated with systemic manifestations, CNS involvement and mild immunodeficiency. This condition is secondary to autosomal recessive mutations of C...

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Detalles Bibliográficos
Publicado en:Pediatr Rheumatol Online J
Main Authors: Caorsi, Roberta, Penco, Federica, Schena, Francesca, Gattorno, Marco
Formato: Artigo
Idioma:Inglês
Publicado: BioMed Central 2016
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5015262/
https://ncbi.nlm.nih.gov/pubmed/27609179
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12969-016-0111-7
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