Carregant...

Monogenic polyarteritis: the lesson of ADA2 deficiency

The deficiency of Adenosine Deaminase 2 (DADA2) is a new autoinflammatory disease characterised by an early onset vasculopathy with livedoid skin rash associated with systemic manifestations, CNS involvement and mild immunodeficiency. This condition is secondary to autosomal recessive mutations of C...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:Pediatr Rheumatol Online J
Autors principals: Caorsi, Roberta, Penco, Federica, Schena, Francesca, Gattorno, Marco
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5015262/
https://ncbi.nlm.nih.gov/pubmed/27609179
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12969-016-0111-7
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!