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Prion protein preamyloid and amyloid deposits in Gerstmann-Sträussler-Scheinker disease, Indiana kindred.

Gerstmann-Sträussler-Scheinker disease (GSS) is a familial neurological disorder pathologically characterized by amyloid deposition in the cerebrum and cerebellum. In GSS, the amyloid is immunoreactive to antisera raised against the prion protein (PrP) 27-30, a proteinase K-resistant peptide of 27-3...

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Dettagli Bibliografici
Autori principali: Giaccone, G, Verga, L, Bugiani, O, Frangione, B, Serban, D, Prusiner, S B, Farlow, M R, Ghetti, B, Tagliavini, F
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1992
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC50124/
https://ncbi.nlm.nih.gov/pubmed/1357663
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