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Hermansky-Pudlak syndrome in the peripartum period

Hermansky-Pudlak syndrome (HPS) is a disease characterized by the triad of oculocutaneous albinism, bleeding diathesis and organ failure secondary to lysosomal accumulation of ceroid lipofuscin. We report the case of a pregnant woman with HPS who had a successful vaginal delivery with the administra...

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Publicado en:Obstet Med
Autores principales: Tong, Iris L, Bourjeily, Ghada
Formato: Artigo
Lenguaje:Inglês
Publicado: SAGE Publications 2008
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4989710/
https://ncbi.nlm.nih.gov/pubmed/27582793
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1258/om.2008.080003
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