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On the origin of 3-methylglutaconic acid in disorders of mitochondrial energy metabolism

3-methylglutaconic acid (3MGA)-uria occurs in numerous inborn errors of metabolism (IEM) associated with compromised mitochondrial energy metabolism. This organic acid arises from thioester cleavage of 3-methylglutaconyl CoA (3MG CoA), an intermediate in leucine catabolism. In individuals harboring...

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Detalhes bibliográficos
Publicado no:J Inherit Metab Dis
Main Authors: Ikon, Nikita, Ryan, Robert O.
Formato: Artigo
Idioma:Inglês
Publicado em: 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4988875/
https://ncbi.nlm.nih.gov/pubmed/27091556
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10545-016-9933-1
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