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Development and Validation of a GC-FID Method for Diagnosis of Methylmalonic Acidemia

BACKGROUND: Urinary organic acids are water-soluble intermediates and end products of the metabolism of amino acids, carbohydrates, lipids, and a number of other metabolic processes. In the hereditary diseases known as organic acidurias, an enzyme or co-factor defect in a metabolic pathway leads to...

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Argitaratua izan da:Rep Biochem Mol Biol
Egile Nagusiak: Keyfi, Fatemeh, Varasteh, Abdolreza
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Varastegan Institute for Medical Sciences 2016
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4986268/
https://ncbi.nlm.nih.gov/pubmed/27536704
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