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Novel pathologic findings in patients with Pelizaeus-Merzbacher disease

Pelizaeus-Merzbacher disease (PMD) is an X-linked inherited hypomyelinating disorder caused by mutations in the gene encoding proteolipid protein (PLP), the major structural protein in central nervous system (CNS) myelin. Prior to our study, whether hypomyelination in PMD was caused by demyelination...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Neurosci Lett
Egile Nagusiak: Laukka, Jeremy J., Kamholz, John, Bessert, Denise, Skoff, Robert P.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2016
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4948744/
https://ncbi.nlm.nih.gov/pubmed/27222925
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.neulet.2016.05.028
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