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Novel pathologic findings in patients with Pelizaeus-Merzbacher disease

Pelizaeus-Merzbacher disease (PMD) is an X-linked inherited hypomyelinating disorder caused by mutations in the gene encoding proteolipid protein (PLP), the major structural protein in central nervous system (CNS) myelin. Prior to our study, whether hypomyelination in PMD was caused by demyelination...

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Detalles Bibliográficos
Publicado en:Neurosci Lett
Main Authors: Laukka, Jeremy J., Kamholz, John, Bessert, Denise, Skoff, Robert P.
Formato: Artigo
Idioma:Inglês
Publicado: 2016
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4948744/
https://ncbi.nlm.nih.gov/pubmed/27222925
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.neulet.2016.05.028
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