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IN VIVO ASSESSMENT OF MUSCLE MEMBRANE PROPERTIES IN MYOTONIC DYSTROPHY

INTRODUCTION: Myotonia in myotonic dystrophy types 1 (DM1) and 2 (DM2) is generally attributed to reduced chloride channel conductance. We used muscle velocity recovery cycles (MVRCs) to investigate muscle membrane properties in DM1 and DM2, with comparisons with myotonia congenita (MC). METHODS: MV...

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Bibliografske podrobnosti
izdano v:Muscle Nerve
Main Authors: Tan, S Veronica, Z’Graggen, Werner J, Boërio, Delphine, Turner, Christopher, Hanna, Michael G, Bostock, Hugh
Format: Artigo
Jezik:Inglês
Izdano: 2016
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC4940227/
https://ncbi.nlm.nih.gov/pubmed/26789642
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/mus.25025
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