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IN VIVO ASSESSMENT OF MUSCLE MEMBRANE PROPERTIES IN MYOTONIC DYSTROPHY
INTRODUCTION: Myotonia in myotonic dystrophy types 1 (DM1) and 2 (DM2) is generally attributed to reduced chloride channel conductance. We used muscle velocity recovery cycles (MVRCs) to investigate muscle membrane properties in DM1 and DM2, with comparisons with myotonia congenita (MC). METHODS: MV...
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| Опубликовано в: : | Muscle Nerve |
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| Главные авторы: | , , , , , |
| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
2016
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| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC4940227/ https://ncbi.nlm.nih.gov/pubmed/26789642 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/mus.25025 |
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