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Familial Hemophagocytic Lymphohistiocytosis due to Mutation of UNC13D Gene

Hemophagocytic lymphohistiocytosis (HLH) are basically a heterogenous group of clinical syndromes, characterised by activation and non-malignant proliferation of benign histiocytes i.e. lymphocytes and macrophages, leading to a cytokine storm that accounts for the fever, organomegaly and multi-organ...

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Dades bibliogràfiques
Publicat a:Indian J Hematol Blood Transfus
Autors principals: Giri, Prabhas Prasun, Biswas, Nirmoy, Chakravarty, Swati
Format: Artigo
Idioma:Inglês
Publicat: Springer India 2015
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4925480/
https://ncbi.nlm.nih.gov/pubmed/27408432
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12288-014-0494-x
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