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Type 1 neurofibromatosis and pulmonary hypertension: a report of two cases and a review

Pulmonary hypertension in type 1 neurofibromatosis is not well known and was previously attributed to diffuse fibrosing alveolitis and parenchymal tumours. More recently, cases of severe pulmonary hypertension due to pulmonary vasculopathy have been described. Involvement of vascular beds, both larg...

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Detalles Bibliográficos
Publicado en:Heart Asia
Autores principales: Malviya, Amit, Mishra, Sundeep, Kothari, Shyam S
Formato: Artigo
Lenguaje:Inglês
Publicado: BMJ Publishing Group 2012
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4898659/
https://ncbi.nlm.nih.gov/pubmed/27326022
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/heartasia-2012-010093
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