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Pulmonary hypertension associated with neurofibromatosis type 2

Although precapillary pulmonary hypertension is a rare but severe complication of patients with neurofibromatosis type 1 (NF1), its association with NF2 remains unknown. Herein, we report a case of a 44-year-old woman who was initially diagnosed with idiopathic pulmonary arterial hypertension and tr...

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Publicado en:Pulm Circ
Autores principales: Taniguchi, Hirohisa, Takashima, Tomoya, Tu, Ly, Thuillet, Raphaël, Furukawa, Asuka, Furukawa, Yoshiko, Kawamura, Akio, Humbert, Marc, Guignabert, Christophe, Tamura, Yuichi
Formato: Artigo
Lenguaje:Inglês
Publicado: SAGE Publications 2021
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC8264739/
https://ncbi.nlm.nih.gov/pubmed/34285798
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/20458940211029550
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