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Decreased N-TAF1 expression in X-linked dystonia-parkinsonism patient-specific neural stem cells

X-linked dystonia-parkinsonism (XDP) is a hereditary neurodegenerative disorder involving a progressive loss of striatal medium spiny neurons. The mechanisms underlying neurodegeneration are not known, in part because there have been few cellular models available for studying the disease. The XDP ha...

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Detalhes bibliográficos
Publicado no:Dis Model Mech
Main Authors: Ito, Naoto, Hendriks, William T., Dhakal, Jyotsna, Vaine, Christine A., Liu, Christina, Shin, David, Shin, Kyle, Wakabayashi-Ito, Noriko, Dy, Marisela, Multhaupt-Buell, Trisha, Sharma, Nutan, Breakefield, Xandra O., Bragg, D. Cristopher
Formato: Artigo
Idioma:Inglês
Publicado em: The Company of Biologists Ltd 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4852502/
https://ncbi.nlm.nih.gov/pubmed/26769797
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.022590
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