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Hypertrophic cardiomyopathy in Friedreich's ataxia.

The cardiac findings in two sibs with Friedreich's ataxia are described. The clinical signs were suggestive of hypertrophic obstructive cardiomyopathy. During left heart catheterization a systolic pressure gradient across the left ventricular outflow tract could be provoked by an infusion of isopren...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Br Heart J
Egile Nagusiak: Van der Hauwaert, L G, Dumoulin, M
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: BMJ Publishing Group 1976
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC483170/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/1034480/
https://ncbi.nlm.nih.govhttps://doi.org/10.1136/hrt.38.12.1291
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