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Cardiomyopathy as the first manifestation of Friedreich's ataxia

We present the case of a female patient diagnosed in childhood with Friedreich Ataxia (FA). At the age of 6, she developed left congestive heart failure with cardiomyopathy, as evident on echocardiogram. Neurologic signs only appeared at age 7, including marked loss of muscle mass, gait instability,...

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Dettagli Bibliografici
Pubblicato in:Autopsy and Case Reports
Autori principali: Rafael Tuzino Leite Neves Maffei, Giulio de los Santos Fortuna, Luca Campolino Rosso, Pedro Dragone Pires, Ivan Rondelli
Natura: Artigo
Lingua:Inglês
Pubblicazione: Hospital Universitário da Universidade de São Paulo 2020
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Accesso online:https://www.redalyc.org/articulo.oa?id=576065838019
https://www.redalyc.org/journal/5760/576065838019/
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https://www.redalyc.org/journal/5760/576065838019/576065838019.epub
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