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Inherited Disorders of Bilirubin Clearance

Inherited disorders of hyperbilirubinemia may be caused by increased bilirubin production or decreased bilirubin clearance. Reduced hepatic bilirubin clearance can be due to defective 1) unconjugated bilirubin uptake and intrahepatic storage, 2) conjugation of glucuronic acid to bilirubin (e.g. Gilb...

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Publicat a:Pediatr Res
Autors principals: Memon, Naureen, Weinberger, Barry I, Hegyi, Thomas, Aleksunes, Lauren M
Format: Artigo
Idioma:Inglês
Publicat: 2015
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4821713/
https://ncbi.nlm.nih.gov/pubmed/26595536
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/pr.2015.247
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