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Cobalt (III) protoporphyrin activates the DGCR8 protein and can compensate microRNA processing deficiency

Processing of microRNA primary transcripts (pri-miRNAs) is highly regulated and defects in the processing machinery play a key role in many human diseases. In 22q11.2 deletion syndrome (22q11.2DS), heterozygous deletion of DiGeorge critical region gene 8 (DGCR8) causes a processing deficiency, which...

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Dettagli Bibliografici
Pubblicato in:Chem Biol
Autori principali: Barr, Ian, Weitz, Sara H., Atkin, Talia, Hsu, PeiKen, Karayiorgou, Maria, Gogos, Joseph A., Weiss, Shimon, Guo, Feng
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4788496/
https://ncbi.nlm.nih.gov/pubmed/26091172
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.chembiol.2015.05.015
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