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The Disease Protein Tulp1 Is Essential for Periactive Zone Endocytosis in Photoreceptor Ribbon Synapses

Mutations in the Tulp1 gene cause severe, early-onset retinitis pigmentosa (RP14) in humans. In the retina, Tulp1 is mainly expressed in photoreceptors that use ribbon synapses to communicate with the inner retina. In the present study, we demonstrate that Tulp1 is highly enriched in the periactive...

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Dades bibliogràfiques
Publicat a:J Neurosci
Autors principals: Wahl, Silke, Magupalli, Venkat Giri, Dembla, Mayur, Katiyar, Rashmi, Schwarz, Karin, Köblitz, Louise, Alpadi, Kannan, Krause, Elmar, Rettig, Jens, Sung, Ching-Hwa, Goldberg, Andrew F. X., Schmitz, Frank
Format: Artigo
Idioma:Inglês
Publicat: Society for Neuroscience 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4764665/
https://ncbi.nlm.nih.gov/pubmed/26911694
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.2275-15.2016
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