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Pentamidine rescues contractility and rhythmicity in a Drosophila model of myotonic dystrophy heart dysfunction

Up to 80% of individuals with myotonic dystrophy type 1 (DM1) will develop cardiac abnormalities at some point during the progression of their disease, the most common of which is heart blockage of varying degrees. Such blockage is characterized by conduction defects and supraventricular and ventric...

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Detalhes bibliográficos
Publicado no:Dis Model Mech
Main Authors: Chakraborty, Mouli, Selma-Soriano, Estela, Magny, Emile, Couso, Juan Pablo, Pérez-Alonso, Manuel, Charlet-Berguerand, Nicolas, Artero, Ruben, Llamusi, Beatriz
Formato: Artigo
Idioma:Inglês
Publicado em: The Company of Biologists 2015
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4728315/
https://ncbi.nlm.nih.gov/pubmed/26515653
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.021428
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