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Endoglin is required in Pax3-Derived Cells for Embryonic Blood Vessel Formation

Mutations in endoglin, a TGFβ/BMP coreceptor, are causal for hereditary hemorrhagic telangiectasia (HHT). Endoglin-null (Eng−/−) mouse embryos die at embryonic day (E)10.5-11.5 due to defects in angiogenesis. In part, this is due to an absence of vascular smooth muscle cell differentiation and vesse...

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Publicat a:Dev Biol
Autors principals: Young, K, Krebs, LT, Tweedie, E, Conley, B, Mancini, M, Arthur, HM, Liaw, L, Gridley, T, Vary, CPH
Format: Artigo
Idioma:Inglês
Publicat: 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4688190/
https://ncbi.nlm.nih.gov/pubmed/26481065
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ydbio.2015.10.019
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