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ALS Patient Stem Cells for Unveiling Disease Signatures of Motoneuron Susceptibility: Perspectives on the Deadly Mitochondria, ER Stress and Calcium Triad

Amyotrophic lateral sclerosis (ALS) is a largely sporadic progressive neurodegenerative disease affecting upper and lower motoneurons (MNs) whose specific etiology is incompletely understood. Mutations in superoxide dismutase-1 (SOD1), TAR DNA-binding protein 43 (TARDBP/TDP-43) and C9orf72, have bee...

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Detalhes bibliográficos
Publicado no:Front Cell Neurosci
Main Authors: Kaus, Anjoscha, Sareen, Dhruv
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4652136/
https://ncbi.nlm.nih.gov/pubmed/26635528
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fncel.2015.00448
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