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Myofibrillar disruption and RNA-binding protein aggregation in a mouse model of limb-girdle muscular dystrophy 1D

Limb-girdle muscular dystrophy type 1D (LGMD1D) is caused by dominantly inherited missense mutations in DNAJB6, an Hsp40 co-chaperone. LGMD1D muscle has rimmed vacuoles and inclusion bodies containing DNAJB6, Z-disc proteins and TDP-43. DNAJB6 is expressed as two isoforms; DNAJB6a and DNAJB6b. Both...

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Bibliografski detalji
Izdano u:Hum Mol Genet
Glavni autori: Bengoechea, Rocio, Pittman, Sara K., Tuck, Elizabeth P., True, Heather L., Weihl, Conrad C.
Format: Artigo
Jezik:Inglês
Izdano: Oxford University Press 2015
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4634370/
https://ncbi.nlm.nih.gov/pubmed/26362252
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddv363
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