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Recurrence of alveolar capillary dysplasia with misalignment of pulmonary veins in two consecutive siblings

Alveolar capillary dysplasia with misalignment of pulmonary veins (ACD/MPV) is a rare, developmental lung disorder, which has been increasingly reported. This entity usually presents as neonatal persistent pulmonary hypertension that is unresponsive to treatment, and is known to be uniformly fatal....

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Publicat a:Autops Case Rep
Autors principals: Benevides, Gabriel Nuncio, Picciarelli de Lima, Patricia, Felipe-Silva, Aloisio, Lovisolo, Silvana Maria, Pereira de Melo, Ana Maria Andrello Gonçalves
Format: Artigo
Idioma:Inglês
Publicat: São Paulo, SP: Universidade de São Paulo, Hospital Universitário 2015
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4608164/
https://ncbi.nlm.nih.gov/pubmed/26484320
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4322/acr.2014.045
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