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Alveolar capillary dysplasia with misalignment of the pulmonary veins: clinical, histological, and genetic aspects

Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACD/MPV) is a rare and lethal disorder mainly involving the vascular development of the lungs. Since its first description, significant achievements in research have led to a better understanding of the underlying molecular mecha...

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Библиографические подробности
Опубликовано в: :Pulm Circ
Главные авторы: Slot, Evelien, Edel, Gabriëla, Cutz, Ernest, van Heijst, Arno, Post, Martin, Schnater, Marco, Wijnen, René, Tibboel, Dick, Rottier, Robbert, de Klein, Annelies
Формат: Artigo
Язык:Inglês
Опубликовано: SAGE Publications 2018
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC6108021/
https://ncbi.nlm.nih.gov/pubmed/30058937
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/2045894018795143
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