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A Novel Syndrome of Generalized Lipodystrophy Associated With Pilocytic Astrocytoma

CONTEXT: A rare presentation of hypothalamic tumors in infants and young children is profound emaciation and generalized loss of sc adipose tissue, also known as “diencephalic syndrome.” Similar loss of sc fat can be observed in children with acquired generalized lipodystrophy or congenital generali...

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Pubblicato in:J Clin Endocrinol Metab
Autori principali: Patni, Nivedita, Alves, Crésio, von Schnurbein, Julia, Wabitsch, Martin, Tannin, Grace, Rakheja, Dinesh, Garg, Abhimanyu
Natura: Artigo
Lingua:Inglês
Pubblicazione: Endocrine Society 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4596037/
https://ncbi.nlm.nih.gov/pubmed/26252356
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/jc.2015-2476
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