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AB083. A cause of cholestasis and hepatic failure in children: neonatal intrahepatic cholestasis cause by citrin deficiency

BACKGROUND AND OBJECTIVE: Neonatal intrahepatic cholestasis caused by citrin deficiency (NICCD) is rare disease. It is a novel metabolism disease which caused by deficiency of citrin, a liver-type mitochondrial aspartate-glutamate carrier encoded by the SLC25A13 gene. Citrin deficiency causes NICCD...

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Foilsithe in:Ann Transl Med
Main Authors: Hoa, Nguyen Pham Anh, Huong, Nguyen Mai, Nhan, Nguyen Thu, Nguyen, Gia Khanh
Formáid: Artigo
Teanga:Inglês
Foilsithe: AME Publishing Company 2015
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Rochtain Ar Líne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4563457/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3978/j.issn.2305-5839.2015.AB083
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