Induced pluripotent stem cell models of Zellweger spectrum disorder show impaired peroxisome assembly and cell type-specific lipid abnormalities

INTRODUCTION: Zellweger spectrum disorder (PBD-ZSD) is a disease continuum caused by mutations in a subset of PEX genes required for normal peroxisome assembly and function. They highlight the importance of peroxisomes in the development and functions of the central nervous system, liver, and other...

全面介紹

Na minha lista:
書目詳細資料
發表在:Stem Cell Res Ther
Main Authors: Wang, Xiao-Ming, Yik, Wing Yan, Zhang, Peilin, Lu, Wange, Huang, Ning, Kim, Bo Ram, Shibata, Darryl, Zitting, Madison, Chow, Robert H., Moser, Ann B., Steinberg, Steven J., Hacia, Joseph G.
格式: Artigo
語言:Inglês
出版: BioMed Central 2015
主題:
Research
在線閱讀:https://ncbi.nlm.nih.gov/pmc/articles/PMC4553005/
https://ncbi.nlm.nih.gov/pubmed/26319495
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13287-015-0149-3
標簽: 添加標簽
沒有標簽, 成為第一個標記此記錄!

相似書籍