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Pulmonary capillary hemangiomatosis: a focus on the EIF2AK4 mutation in onset and pathogenesis

Pulmonary capillary hemangiomatosis (PCH) is a pulmonary vascular disease that mainly affects small capillaries in the lung, and is often misdiagnosed as pulmonary arterial hypertension or pulmonary veno-occlusive disease due to similarities in their clinical presentations, prognosis, and management...

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Detalhes bibliográficos
Publicado no:Appl Clin Genet
Main Authors: Ma, Lijiang, Bao, Ruijun
Formato: Artigo
Idioma:Inglês
Publicado em: Dove Medical Press 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4536836/
https://ncbi.nlm.nih.gov/pubmed/26300654
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2147/TACG.S68635
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