Carregant...

Gaucher Disease: The Metabolic Defect, Pathophysiology, Phenotypes And Natural History

Gaucher disease (GD), a prototype lysosomal storage disorder, results from inherited deficiency of lysosomal glucocerebrosidase due to biallelic mutations in GBA. The result is widespread accumulation of macrophages engorged with predominantly lysosomal glucocerebroside. A complex multisystem phenot...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:Pediatr Endocrinol Rev
Autors principals: Baris, Hagit N., Cohen, Ian J., Mistry, Pramod K.
Format: Artigo
Idioma:Inglês
Publicat: 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4520262/
https://ncbi.nlm.nih.gov/pubmed/25345088
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!