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Temperature-sensitive retinoid isomerase activity of RPE65 mutants associated with Leber Congenital Amaurosis

RPE65 is a membrane-associated retinoid isomerase involved in the visual cycle responsible for sustaining vision. Many mutations in the human RPE65 gene are associated with distinct forms of retinal degenerative diseases. The pathogenic mechanisms for most of these mutations remain poorly understood...

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Dades bibliogràfiques
Publicat a:J Biochem
Autors principals: Li, Songhua, Hu, Jane, Jin, Robin J., Aiyar, Ashok, Jacobson, Samuel G., Bok, Dean, Jin, Minghao
Format: Artigo
Idioma:Inglês
Publicat: Oxford University Press 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4516983/
https://ncbi.nlm.nih.gov/pubmed/25752820
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/jb/mvv028
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