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ALS mutant FUS proteins are recruited into stress granules in induced pluripotent stem cell-derived motoneurons

Patient-derived induced pluripotent stem cells (iPSCs) provide an opportunity to study human diseases mainly in those cases for which no suitable model systems are available. Here, we have taken advantage of in vitro iPSCs derived from patients affected by amyotrophic lateral sclerosis (ALS) and car...

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Dettagli Bibliografici
Pubblicato in:Dis Model Mech
Autori principali: Lenzi, Jessica, De Santis, Riccardo, de Turris, Valeria, Morlando, Mariangela, Laneve, Pietro, Calvo, Andrea, Caliendo, Virginia, Chiò, Adriano, Rosa, Alessandro, Bozzoni, Irene
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Company of Biologists 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4486861/
https://ncbi.nlm.nih.gov/pubmed/26035390
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.020099
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