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A rare cause of thrombocyte dysfunction: Hermansky-Pudlak syndrome

Hermansky-Pudlak syndrome (HPS) is an autosomal recessive disease characterized with oculocutaneous albinism and platelet aggregation disorder. The clinical picture is highly variable and patients may present with different complaints., Ecchymoses usually develop in childhood; epistaxis, postoperati...

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Опубликовано в: :Turk Pediatri Ars
Главные авторы: Özdemir, Nihal, Çelik, Emre, Başlar, Zafer, Celkan, Tiraje
Формат: Artigo
Язык:Inglês
Опубликовано: Turkish Pediatrics Association 2014
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC4462281/
https://ncbi.nlm.nih.gov/pubmed/26078655
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.5152/tpa.2014.1071
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