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Analysis of CFTR Folding and Degradation in Transiently Transfected Cells

Misfolding and premature degradation of F508del-CFTR is the major cause of cystic fibrosis. Components of the ubiquitin-proteasome system function on the surface of the endoplasmic reticulum to select misfolded proteins for degradation. The folding status of F508del-CFTR is monitored by at least two...

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Pubblicato in:Methods Mol Biol
Autori principali: Grove, Diane E., Rosser, Meredith F.N., Watkins, Richard L., Cyr, Douglas M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2011
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4460993/
https://ncbi.nlm.nih.gov/pubmed/21594788
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/978-1-61779-117-8_15
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