Lung MRI and impairment of diaphragmatic function in Pompe disease

BACKGROUND: Pompe disease is a progressive metabolic myopathy. Involvement of respiratory muscles leads to progressive pulmonary dysfunction, particularly in supine position. Diaphragmatic weakness is considered to be the most important component. Standard spirometry is to some extent indicative but...

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Detalhes bibliográficos
Publicado no:BMC Pulm Med
Main Authors: Wens, Stephan CA, Ciet, Pierluigi, Perez-Rovira, Adria, Logie, Karla, Salamon, Elizabeth, Wielopolski, Piotr, de Bruijne, Marleen, Kruijshaar, Michelle E, Tiddens, Harm AWM, van Doorn, Pieter A, van der Ploeg, Ans T
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2015
Assuntos:
Research Article
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4428089/
https://ncbi.nlm.nih.gov/pubmed/25943437
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12890-015-0058-3
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